• It is the most common malignant intraocular tumor of childhood.
• It is more common in the first two years. 30% is bilateral, 20% is autosomal dominant.
• Calcification can be seen at a rate of 70% in radiological examinations.
• It is the most important cause of leukocoria in newborns.
• Hereditary tumors are characteristically multicentric.
• Osteosarcoma accompanies the secondary tumors most frequently.
• Flexner - Wintersteiner badges appear characteristically.
The most common primary benign intraorbital tumor is capillary hemangioma in children and cavernous hemangioma in adults.
The most common primary malignant intraorbital tumor is rhabdomyosarcoma in children and malignant melanoma in adults.
The most common primary malignant intraocular tumor is retinoblastoma in children and malignant melanoma in adults.